Definition: presence of tumors in at least two functionally independent endocrine glands.
Autosomal dominant
Complete penetrance by 70 years old.
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- MEN1 (Wermer Syndrome) - skin findings similar to tuberous sclerosis
- MEN2A (Sipple Syndrome) - amiloidosis childhood onset
- MEN2B (Gorlin Syndrome) - multiple mucosal neuromas