DermWiki

O DermWiki nasceu dos meus resumos de preparação para o exame final de internato — notas pessoais que, com o tempo, percebi poderem ser úteis a outros. Este projeto que assenta na ideia maior de comunidade e de que o conhecimento médico cresce quando é partilhado. Se encontrares algum erro, tiveres uma perspetiva diferente ou quiseres contribuir, entra em contacto — a comunidade dermatológica constrói-se assim, de médico para médico.
João Nuno Soares (jonubaso@gmail.com)
 
Generalidades
Lesões Elementares Dermatológicas
 
 
 
 
 
 
  • Doenças Anexiais
    • Unidade foliculosebácea
      • Folículo piloso
        💡
        O corpo humano tem aproximada 5 milhões de folículos, incluindo 100.000 a 150.000 que estão no couro cabeludo
        Hair Follicle Embryology
        • O pelo na embriologia surge por proliferação de celulas basais que se chama germe folicular no 3o mes de vida e formam um gomo semelhante aos ninhos de celulas basaloides do CBC
          • As glandulas apocrinas e sebaceas tem origem na mesma unidade
        • Follicles evident at 9 weeks gestation on brow, chin and lips
        • Body hair (lanugo) evident at 4 months in fetus
        • Lanugo hairs shed at 7-8 mos; no new follicles formed after birth
        • Follicle types
          • Lanugo: soft, lightly pigmented, unmedullated, present in aduls only in pathologic states
          • Vellus: fine, non-pigmented, unmedullated
          • Terminal: coase, pigmented, medullated
         
        Hair follicle development
        • Dermal mesenchyme signals overlying epithelium to thicken and form placode
        • Clustering of mesenchyme and formation of a dermal condensate
        • Second dermal signal causes epidermis invasion into dermis forming hair germ then hair peg and bulbous peg
        • Condensate becomes dermal papila
        • Genes WNT and Beta-catenina: important for dermal signal for follicle development
          • notion image
         
         
        Normal Hair cycling
        • Air follicle activity is cyclical
        • Humans undergo about 10-30 cycles throughout their lifetimes
        • In childhood, all hairs on the scalp are in sync and shed at the same time but eventually cycles become asynchronous
        • Hair is replaced every 3-5 years
        • At any given time 85-90% of hairs are in anagen, 10-15% in telogen and 1% in categen
        • On 100.000 hair scalp: 13.000 are in telogen and the cycle last 3 months leading to loss of 100-144 hairs per day
        • Anagénese demora 3 a 10 anos no couro cabeludo, 4 a 14 semanas no bigode)
        • O cabelo cresce aproximadamente 0,35mm/dia
         
        Estrutura do cabelo
        • Queratinas do folículo piloso - 2 tipos predominantes
          • Acidic keratin cluster (type I)
            • 17q12-q21
            • K31-40
          • Basic keratin cluster (type II)
            • 12q11-q13
            • K81-86
         
        Camadas do folículo piloso
        • Sentido de crescimento das células
          • As celulas da parte mais profunda queratinizam no sentido vertical para formar a haste pilosa
          • As células da parte mais superficial queratinizam no sentido horizontal para revestir o lúmen do folículo piloso
        • Secção longitudinal
          • Esquema
            notion image
            notion image
          • Infundíbulo
            • Queratinização = epiderme interfolicular
            • uppermost part
            • Greatest inflammation in cicatricial alopecias
            • From the junction with interfollicular epidermis to opening of sebaceous gland
          • Istmo
            • Desde a abertura da glândula sebácea e apócrina até ao músculo eretor do pelo
            • Trichilemmal Keratinization
              • Assentada basal
              • Depois as celulas em vez de achatarem vão aumentado de volume e o citoplasma vai ficando mais palido em direção ao eixo do folículo piloso.
              • Não existe granulosa
              • Camada cornea é eosinofílica.
              • Isto reproduz o que vemos nos quistos triquilémico que chamamos catagénicos
              • abnormal in congenital atrichia with papules (due to hairless and vitamin D receptor genes mutation)
              • Also greatest inflammation in cicatricial alopecias
          • Bulge
            • lowest part of the hair follicle that does not regress during the catagen phase
            • where stem cells are
            • cell at the bulb also replicate and have properties of stem cells, except they regress along with the rest of the lower follicle during catagen
          • Stem
            • Celulas mais claras, a basal não é tão basofílica, membrana é mais evidente
          • Matriz (bolbo)
            • Celulas mais pequenas, condensas, tem pigmento devido a melanina produzida por melanócitos que também existem
            • greatest activity and inflammation in alopecia areata
        • Secção horizontal ou transversal
          • Esquema
            notion image
          • Hair shaft
            • Hair shaft medulla (central portion)
            • Hair shaft cortex (forms the bulk of the hair shaft)
              • Cortex and Medulla - responsible for strength of hair shaft
            • Hair shaft cuticle (protective layer)
              • Cuticle - outermost part of hair shaft, responsible for aesthetic appearence
          • Inner root sheath
            • The inner root sheath cuticle
            • Huxley’s layer
            • Henle’s layer
          • Outer root sheath → continuous with the epidermis (basal+spinosum layers)
            • Stratum basale
            • Stratum spinosum
         
        Pigmentação do Folículo Piloso
        • Melanosomes in the hair cortex are larger than epidermal melanosomes. There are two main melanin types
          • Phomelanin (red/yellow)
            • Pigment abundant in redheads. Common in individuals with recessive mutation in MC1R (predisposed to melanoma)
          • Eumelanin (black/brown)
            • Blonde hair is created by low levels of eumelanin NOT high levels of pheomelanin and accordingly browns with age. Natural blonde hair in adulthood is very rare (2%)
            • Graying - reduction of tyrosinase in hair bulb and melanocyte damage due to reactive O2 species
            • By age 50, 50% of people have at least 50% of gray hair
         
        Hair differences between ethnic groups
        Parameter
        Asian
        Caucasian
        African
        Growth rate (um/day)
        411 (because more straight)
        367
        280 (because more curly)
        Hair density (hairs/cm2)
        175
        226
        161
        Ellipticity (cross section)
        90% (circular) - straight
        75% (less circular)
        60 (oval) - curly
         
        Effects of Medications
        • Estrogens reduce hair growth rate and prolong anagen
          • Estrogens responsible for prolonged anagen state in pregnancy
        • Androgens increase hair growth rate and hair diameter (in androgen-dependent sites)
          • but decrease hair density in Androgenic alopecia
          • Hirsutism
        • Thyroxine promotes growth
        • Corticosteroids retard/slow anagen onset
          • Keep in mind when treating patients with inflammatory alopecia with corticosteroids, stop when inflammation is no longer present
        Glândulas sebáceas
        • Funções
          • Secreção holócrina → sebo
            • Marcador de atividade androgénica
              • notion image
          • Síntese de androgénios
          • Modulação imune
        • Microbiota
          • Malassezia
          • Saphylococcus epidermidis
          • Cutibacterium
          • Demodex
        • Ativação: androgénios (DHT)
        • Histologia
          • Forma piriforme
          • Porção excretora
            • Drenar no folículo que tem uma pequena diferença em relação ao folicular porque tem porção com estrutura crenada (os verdadeiros quistos sebaceos têm isso)
              • Glândulas sebáceas ectópicas livres (exceção)
                • Vermilion dos lábios → fordyce spots or granules
                • Labia minora and prepuce → Tyson glands
                • Aréola - Montgomery tubercles
                • Pálpebras → meibomian glands
        Doenças das glândulas sebáceas
        notion image
        🗻
        Acne
        ❤️‍🔥
        Rosácea
        🚬
        Hidradenite Supurativa | Verneuil’s Disease | Acne Inversa
        Follicular Occlusion Tetrad
    • Glândulas sudoríparas écrinas e apócrinas
      • Glândulas apócrinas
        • Glândulas apócrinas
          • Localização: axila, anogenital, periumbilical, areola dos mamilos, bordo vermilion dos lábios
          • Secreção de fluido estéril, sem odor, viscoso que é rico em precursores de substâncias odorífaras
            • Em animais: feromonas, respostas comportamentais, atração sexual, marcar território
            • Em humanos: comunicação olfativa
          • Ativação: androgénio dependentes
          • Formas modificadas de glandulas apócrinas
            • Glândulas ceruminous: canal auditivo externo
            • Glândulas Moll: margem palpebral
          • Histologia
            • Porção secretora
              • Camada única de células colunares envolvida por células mioepiteliais
              • Na derme profunda e gordura subcutânea
              • Secreção por decapitação (as sebáceas é por secreção holócrina)
            • Porção ductal
              • Dupla camada de células cuboides com camada mioepitelial
              • Porção apical (acrisyringium) drena para folículo terminal
          • Desenvolvimento
            • Deriva da unidade foliculo-sebácea
            • Presentes em todo o tegumento no embrião, mas algumas desaparecem
            • Aumentam na puberdade por estimulação androgénica
              • notion image
        • Poromas habitualmente são denominados écrinos, mas há autores que defende que são apócrinos
        Glândulas écrinas
        • Glândulas écrinas
          • Localização: disseminada.
            • Maior densidade palmoplantar
            • Exceto: pele do cana auditivo externo, vermilion dos lábios, clitoris, labia minora, glande do pénis
          • Ativação: estímulo colinérgico (sistema nervoso simpático): emocional e térmico. Função termorreguladora.
          • Secreção: secreção eletrolítica
            • Estimulação máxima: 3L em 1h (hiperhidrose palmoplantar)
            • Excreção de medicamentos no stratum corneum (ex. fluconazol, chemotherapy → neutrophilic eccrine hidradenitis)
            • Contém peptidos antimicrobianos
          • Histologia
            • Não há grandes diferenças histológicas entra a porção excretora das glândulas apócrina e ecrina
              • notion image
            • Porção secretora: camada celular única com 2 tipos de células
              • Células grandes claras secretoras
              • Células escuras de função desconhecia com granulos basofílicos
              • Rodeados por camada mioepitelial
            • Porção ductal: 2 ou mais camadas de células cuboides sem mioepitélio envolvente
              • Porção apical (acrosyringium) drena diretamente para a pele
              • Porção intraepidérmica do ducto enroscada em saca rolhas
          • Desenvolvimento
            • Independente do folículo pilosebáceo
            • notion image
        Imunohistoquímica glandulas ecrinas
        • sox10
        🌊
        Hiperhidrose écrina
        Apocrine Chromhidrosis
        Eccrine chromhidrosis and bromhidrosis
        Neutrophilic Eccrine Hidradenitis
       
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
Outros
🏥
Dermatologia Urgência
🛌
Internamento
Consulta de Imunossupressão
Research
 
 
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