Benign Cephalic Histiocytosis

  • Children <3yo
  • Red to brown 2-5mm papules on head/neck first, sometimes rest of body
  • Spontaneous resolution over months/years
  • Pathology
    • Well-circumscribed dermal infiltrate of large histiocytes (non-lipid), eosinophilic cytoplasm, intracytoplasmic comma bodies (Eletron Microscopy)
    • Factor XIIIa, CD68 positive; CD1a, S100 negative