Dermatoses do Umbigo

Anatomia do Umbigo
  • Margem: anel umbilical
  • Goteira umbilical → prega - dermatoses intertriginosas
  • Monte umbilical
 
Developmental abnormalities
  • Persistence of the urachal canal
    • Urine leak
    • Failure of urachus to close
  • Persistence of the omphalomesenteric duct
    • Omphalitis
    • Fecal matter elimination
    • Polyps
    • Botryomycoma
    • Presence of sterile umbilical serosity
    • Histology → intestinal mucosa
 
Tumors (benign and malignant) and pseudotumors
notion image
  • Omphalocele → umbilical hernia
  • Foreign bodies
    • Rare
    • Talc granulomas in the past
  • Omphaloliths or omphalokeratoliths
    • Chalky concretions that can go unnoticed for years, only becoming apparent in the event of inflammation, infection or ulceration
  • Umbilical polyps
    • Suggests a developmental abnormality
  • Endometrioma umbilical
    • Endometriose: presença de tecido endometrial funcional (hormono-dependente) fora da cavidade uterina
    • Envolvimento cutâneo em 1%
    • Painless, firm, non-ulcerated, blue-black tumor of varying size with possible bloody discharge in sync with the menstrual cycle
    • Abordagem: U/S or MRI
    • Tratamento: cirúrgico
  • Umbilical metastases
      • Sister Mary Joseph Nodule
        • ++ women 50-70yo
        • Gastric carcinoma > colon carcinoma > ovarian > pancreatic carcinoma > endometrial
        • Histology: adenocarcinoma >> carcinoid
        • First manifestation in 15-50%
        • When no primary is found: considered primary degeneration of embryonic remnants
  • Primary tumors
    • Adenocarcinoma of urachus
    • Basal cell carcinoma
    • Squamous cell carcinoma
    • Melanoma
    • Extra mammary Paget Disease
 
Inflammatory
Omphalitis (syndrome)
 
Other lesions
  • Navel pulled upward during pregnancy and downward during ascitis
  • Bluish or yellowish discoloration (Cullen’s sign) → if hemoperiteneum (ectopic pregnancy), acute pancreatitis, after liver biopsy
  • Absence of umbilicus → congenital dystrophic epidermolysis bullosa